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KMID : 1039920170240010040
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Neonatal Medicine
2017 Volume.24 No. 1 p.40 ~ p.44
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A Case of Congenital Lymphatic Dysplasia Complicated by Hydrops Fetalis
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Yoon Young-Mi
Kim Seon-Nyo
Kim Hye-Rim
Jung Young-Hwa
Choi Chang-Won
Kim Beyong-Il
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Abstract
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Congenital lymphatic dysplasia is a rare congenital maldevelopment of the lymphatic system, in which dysfunction of the lymphatic system may cause leakage of lymph fluid into the limbs and the pleural, pericardial, or peritoneal cavity. We experienced a case of hydrops fetalis with subcutaneous lymphedema, chylothorax, chylous ascites and pericardial effusion. Lymphangiography revealed a critical defect of lymphatic system. Here, we report the first case of premature infant with congenital lymphatic dysplasia confirmed by lymphangiography, which is the first reported in Korea.
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KEYWORD
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Congenital lymphatic dysplasia, Lymphangiography, Hydrops fetalis
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